Maple syrup urine disease.
This 9-month-old infant with classic type maple syrup urine disease suffered an acute decompensation following a viral illness. A. There is abnormal hyperintensity in the globi pallidi and internal capsules on this T2-weighted MR image. B. A diffusion-weighted image shows hyperintensity in the internal capsules, globi pallidi, cerebral peduncles, and brainstem.