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Chapter 27

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1. Microphthalmia

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Figure 27-1

Microphthalmia.

There is severe left-sided microphthalmia on this unenhanced axial CT image of a 3-week-old infant. The sclera (arrow) is slightly hyperattenuating relative to adjacent soft tissues. There is no discernible lens. The optic nerve complex is small.

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2. Retinochoroidal coloboma

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Figure 27-2

Retinochoroidal coloboma.

A, B. Fat-suppressed T2-weighted (A) and standard T1-weighted (B) MR images show a retrobulbar right orbital cyst (arrows). The globe is slightly small and distorted.

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3. Microphthalmos with cyst

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Figure 27-3

Microphthalmos with cyst.

A coronal T1-weighted MR image shows a large right orbital cyst (C) inferior to a small dysplastic globe (arrow).

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4. Morning glory disk anomaly

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Figure 27-4

Morning glory disk anomaly.

An axial T2-weighted MR image of a 3-month-old child shows a choroidoscleral defect at the optic nerve head and posterior extension of vitreous through the defect (arrow). This child also slight ectasia of the optic nerve sheath.

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5. Buphthalmos

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Figure 27-5

Buphthalmos.

A contrast-enhanced T1-weighted MR image of a child with NF-1 shows an enlarged left globe. There is an enhancing infiltrative plexiform neurofibroma in the left orbit, periorbital region, and infratemporal fossa. The bony walls of the orbit are expanded. Exophthalmos is due to the enlarged globe and globe displacement by the neurofibroma.

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6. Persistent hyperplastic primary vitreous

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Figure 27-6

Persistent hyperplastic primary vitreous.

A. Contrast-enhanced CT shows increased attenuation in a small right globe. There is triangular enhancing soft tissue extending through the central aspect of the vitreous chamber. B. Subretinal fluid is hyperintense on this T1-weighted MR image. Fibrovascular tissue between the displaced retinal leaves has a triangular shape. The anterior chamber is small.

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7. Coats disease

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Figure 27-7

Coats disease.

There is abnormal increased attenuation throughout the vitreous of the left globe on this contrast-enhanced CT image of a 2-year-old child with leukocoria. There is mild microphthalmos.

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8. Choroidal venous angioma

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Figure 27-8

Choroidal venous angioma.

A. An axial fat-suppressed T1-weighed image of a 7-year-old child with a left facial port-wine stain shows high signal intensity subretinal fluid collections in the left globe. The choroidal ...

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