RT Book, Section
A1 Hawkins, Douglas S.
A1 Spunt, Sheri L.
A2 Kline, Mark W.
SR Print(0)
ID 1182911383
T1 Rhabdomyosarcoma and Other Soft Tissue Sarcomas
T2 Rudolph's Pediatrics, 23e
YR 2018
FD 2018
PB McGraw-Hill Education
PP New York, NY
SN 9781259588594
LK accesspediatrics.mhmedical.com/content.aspx?aid=1182911383
RD 2024/04/19
AB The  World  Health  Organization  divides  soft  tissue  tumors  into  4  categories  based  on  clinical  behavior:  benign,  intermediate  (locally  aggressive),  intermediate  (rarely  metastasizing),  and  malignant.  Benign  soft  tissue  tumors  such  as  lipoma,  nodular  fasciitis,  and  hemangioma  predominate  in  pediatric  patients.  Certain  intermediate-behavior  soft  tissue  tumors,  including  desmoid-type  fibromatosis  and  dermatofibrosarcoma  protuberans,  occur  frequently  in  childhood.  The  more  than  30  histologic  subtypes  of  malignant  soft  tissue  tumors  comprise  approximately  7%  of  all  cancers  among  children  and  adolescents.  In  children,  rhabdomyosarcoma  (RMS)  is  by  far  the  most  common  soft  tissue  sarcoma,  accounting  for  about  40%  of  cases.  Because  RMS  predominates,  the  remaining  malignant  soft  tissue  tumors  are  often  referred  to  as  non-rhabdomyosarcoma  soft  tissue  sarcoma  (NRSTS).