RT Book, Section
A1 Orenstein, David M.
A2 Rudolph, Colin D.
A2 Rudolph, Abraham M.
A2 Lister, George E.
A2 First, Lewis R.
A2 Gershon, Anne A.
SR Print(0)
ID 7051780
T1 Chapter 514. Cystic Fibrosis
T2 Rudolph's Pediatrics, 22e
YR 2011
FD 2011
PB The McGraw-Hill Companies
PP New York, NY
SN 978-0-07-149723-7
LK accesspediatrics.mhmedical.com/content.aspx?aid=7051780
RD 2024/04/24
AB Cystic  fibrosis  (CF)  is  the  most  common  profoundly  life-shortening  inherited  disease  in  North  America.  In  1938,  Dr.  Dorothy  Andersen  first  described  the  complex  of  respiratory  and  digestive  signs  and  symptoms  that  make  up  this  syndrome,1  but  references  to  a  childhood  disorder  characterized  by  salty  sweat  and  early  death  date  back  to  at  least  the  Middle  Ages.  The  cellular  and  molecular  bases  for  the  disorder  have  recently  been  elucidated.2,3