Sections View Full Chapter Figures Tables Videos Full Chapter Figures Tables Videos Supplementary Content +++ Key Features ++ Characterized by failure of segmentation of some or all of the cervical vertebrae Multiple congenital spinal anomalies may be present, with hemivertebrae and scoliosis among the most common presentations +++ Clinical Findings ++ Short and stiff neck Low hairline Low set ears Associated defects Cervical rib Spina bifida Torticollis Web neck High scapula Renal anomalies Deafness +++ Diagnosis ++ Renal ultrasound Hearing test +++ Treatment ++ Surgical intervention is necessary to prevent neurologic injury in symptomatic patients with unstable spinal anomalies If asymptomatic, a spine surgeon will determine if surgical intervention is warranted after review of patient's age, history, and activity level Spinal arthrodesis is indicated if progressive scoliotic deformities develop GET ACCESS TO THIS RESOURCE Sign In Username Error: Please enter User Name Password Error: Please enter Password Forgot Username? Forgot Password? Sign in via OpenAthens Sign in via Shibboleth Get Free Access Through Your Institution Contact your institution's library to ask if they subscribe to McGraw-Hill Medical Products. Access My Subscription GET ACCESS TO THIS RESOURCE Subscription Options Pay Per View Timed Access to all of AccessPediatrics 24 Hour $34.95 (USD) Buy Now 48 Hour $54.95 (USD) Buy Now Best Value AccessPediatrics Full Site: One-Year Individual Subscription $595 USD Buy Now View All Subscription Options