Sections View Full Chapter Figures Tables Videos Annotate Full Chapter Figures Tables Videos Supplementary Content +++ Key Features ++ Characterized by failure of segmentation of some or all of the cervical vertebrae Multiple congenital spinal anomalies may be present, with hemivertebrae and scoliosis among the most common presentations +++ Clinical Findings ++ Short and stiff neck Low hairline Low set ears Associated defects Cervical rib Spina bifida Torticollis Web neck High scapula Renal anomalies Deafness +++ Diagnosis ++ Renal ultrasound Hearing test +++ Treatment ++ Surgical intervention is necessary to prevent neurologic injury in symptomatic patients with unstable spinal anomalies If asymptomatic, a spine surgeon will determine if surgical intervention is warranted after review of patient's age, history, and activity level Spinal arthrodesis is indicated if progressive scoliotic deformities develop Your Access profile is currently affiliated with [InstitutionA] and is in the process of switching affiliations to [InstitutionB]. Please select how you would like to proceed. Keep the current affiliation with [InstitutionA] and continue with the Access profile sign in process Switch affiliation to [InstitutionB] and continue with the Access profile sign in process Get Free Access Through Your Institution Learn how to see if your library subscribes to McGraw Hill Medical products. Subscribe: Institutional or Individual Sign In Error: Incorrect UserName or Password Username Error: Please enter User Name Password Error: Please enter Password Sign in Forgot Password? Forgot Username? Sign in via OpenAthens Sign in via Shibboleth You already have access! Please proceed to your institution's subscription. Create a free profile for additional features.