A spectrum of epidermal nevi may be represented in this syndrome:
verrucous epidermal nevus, nevus sebaceus, wooly hair nevus, Becker
nevus, and nevus comedonicus. Other mucocutaneous lesions include
hypo- or hyperpigmentation, café au lait macules, hemangiomas,
aplasia cutic congenita, hair and dental abnormalities, and dermatomegaly
(increase in skin thickness, warmth, and hairiness).
Associated systemic abnormalities may be seen in the CNS (hemimegalencephaly,
seizures, hemiparesis, mental retardation), skeleton (bone deformities,
cysts, atrophies, and hypertrophies), ocular, cardiac, and/or
GU system.