TY - CHAP M1 - Book, Section TI - Primary Immunodeficiency Diseases A1 - Butte, Manish J. A1 - Walter, Jolan E. A2 - Zaoutis, Lisa B. A2 - Chiang, Vincent W. PY - 2017 T2 - Comprehensive Pediatric Hospital Medicine, 2e AB - If diagnosed in a timely fashion and monitored adequately, patients with primary immunodeficiency diseases (PIs) infrequently require hospitalization for treatment of infections, flares of autoimmunity, and rarely, management of cancer. The greatest challenge is making an expeditious diagnosis of a PI. Initial evaluation often occurs during a hospitalization for prolonged, severe, or recurrent infections. Occasionally, illnesses due to unusual pathogens raise suspicion for an underlying immunodeficiency. Thus increased awareness of the key features of PIs not only assists in management of these children when admitted, but also helps the pediatric hospitalist identify children at risk for PI. In most cases, these children benefit when the hospitalist can promptly initiate appropriate laboratory studies and obtain consultation from a pediatric immunologist. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/04/23 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1146114882 ER -