TY - CHAP M1 - Book, Section TI - Disorders of Glycogen Metabolism A1 - Kishnani, Priya S. A1 - Chen, Yuan-Tsong A2 - Kline, Mark W. PY - 2018 T2 - Rudolph's Pediatrics, 23e AB - Glycogen, the storage form of glucose in animal cells, is composed of glucose residues joined in straight chains by α–1,4 linkages and branched at intervals of 4 to 10 residues with α–1,6 linkages. The tree-like molecule can have a molecular weight of many millions and may aggregate to form structures recognizable by electron microscopy. In muscle, glycogen forms β particles, which are spherical and contain up to 60,000 glucose residues. Each β particle contains a covalently linked protein called glycogenin. Liver contains β particles and rosettes of glycogen called α particles, which appear to be aggregated β particles. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/28 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1182929181 ER -