TY - CHAP M1 - Book, Section TI - Epidermolysis Bullosa A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas PY - 2019 T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - It is defined as a group of genetically inherited connective tissue disorders characterized by cutaneous blistering of the skin and mucosal membranes after minor trauma. The lesions heal with severe scarring. It results from a membrane defect located between the epidermis and the dermis as a result of external shearing forces applied to the skin, such as simple friction. Its severity ranges from mild to lethal. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/28 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1164069017 ER -