TY - CHAP M1 - Book, Section TI - Fibrin Stabilizing Factor (Factor XIII) Deficiency A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas PY - 2019 T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - Inherited coagulation disorder resulting in life-long bleeding tendency in homozygotes with poor wound healing and easy bruising. The presence of severe bleeding diathesis is characterized by recurrent soft tissue bleeding, poor wound healing, and a high incidence of intracranial hemorrhage. The presence of normal coagulation screening tests, including prothrombin time (PT), partial thromboplastin time (PTT), fibrinogen level, platelet count, and bleeding time and a history of severe bleeding diathesis should be considered a Factor XIII deficiency until proven otherwise. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/29 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1164070048 ER -