TY - CHAP M1 - Book, Section TI - Gaucher Disease A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas PY - 2019 T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - Most common inherited lipid storage disease. It is particularly common in Ashkenazi Jewish people. Characterized by accumulation of glucocerebrosides (derived from red blood cells) in many tissues, especially the macrophages in the bone marrow. Attention should be given to hematological parameters in particular with children with mild, nonneuronopathic Type I and severe neuronopathic Type III Gaucher disease in an attempt to minimize postoperative bleeding, the most serious complication. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/10/07 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1164070585 ER -