TY - CHAP M1 - Book, Section TI - Gorlin-Goltz Syndrome A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas PY - 2019 T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - Autosomal dominant inherited ectodermal disorder characterized by basal cell nevi on the torso and shoulders with a potential of malignant degeneration. Gorlin-Goltz Syndrome is an autosomal dominant inherited disorder characterized by the presence of multiple odontogenic keratocysts along with various cutaneous, dental, osseous, ophthalmic, neurological, and sex organ abnormalities. Early diagnosis is essential as it may progress to aggressive basal cell carcinomas and neoplasias. Multiple cysts of variable size can be found in the maxilla, mandible and airway, and may make endotracheal intubation difficult. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/28 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1164071456 ER -