TY - CHAP M1 - Book, Section TI - Kashani-Strom-Utley Syndrome A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas PY - 2019 T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - Polymalformative syndrome characterized by hypoplastic pulmonary arteries and aorta and urinary tract malformations. Predisposing factors include cigarette smoking, recurrent or chronic respiratory infections, air pollution, occupational exposure to chemicals, and allergies. Smoking is by far the most important of these factors—it impairs ciliary action and macrophage function, inflames airways, increases mucus production, destroys alveolar septae, and causes peribronchiolar fibrosis. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/28 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1164074802 ER -