TY - CHAP M1 - Book, Section TI - Microvillous Inclusion Syndrome A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas PY - 2019 T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - It is an extremely rare inherited enteropathy that is typically apparent within hours or days after birth. The disorder is characterized by chronic, severe, watery diarrhea, and malabsorption caused by hypoplasia and/or atrophy of the wall of the small intestine (eg, hypoplastic villus atrophy, defective brush-border assembly and differentiation). In infants, chronic diarrhea and malabsorption may result in severe dehydration, electrolyte imbalance, malnutrition, failure to thrive, and acidosis. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/28 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1164078693 ER -