TY - CHAP M1 - Book, Section TI - Mucopolysaccharidosis (MPS) A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas PY - 2019 T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - It is a large spectrum of disease defined as a metabolic storage condition that affects multiple organs. They are characterized by the absence or malfunctioning of lysosomal enzymes that normally metabolize the glycosaminoglycans. This enzyme is responsible for the lubrification of all tissues, eg, articulations. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/29 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1164079399 ER -