TY - CHAP M1 - Book, Section TI - Rett Syndrome (RTS) A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas PY - 2019 T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - A severe and global developmental disorder affecting the central nervous system (CNS) characterized by autism, dementia, ataxia, and loss of purposeful use of the hand. It is known as a uniform and striking progressive encephalopathy. Evolution in four phases after diagnosis is typical. Cardiac, respiratory, and gastrointestinal (GI) signs are associated. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/04/19 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1164083595 ER -