TY  - CHAP
M1  - Book, Section
TI  - Hereditary Hemorrhagic Telangiectasia
A1  - Bissonnette, Bruno
A1  - Luginbuehl, Igor
A1  - Engelhardt, Thomas
Y1  - 2019
N1  - 
T2  - Syndromes: Rapid Recognition and Perioperative Implications, 2e
AB  - Autosomal  dominant  mucocutaneous  and  visceral  fibrovascular  dysplasia  in  which  telangiectasia,  arteriovenous  malformations,  and  vascular  aneurysms  may  be  widely  distributed  throughout  the  cardiovascular  system.  It  is  usually  recognized  as  a  “triad”  of  telangiectasia,  recurrent  epistaxis,  and  a  family  history  of  the  disorder.  The  telangiectasias  are  located  on  the  skin  and  mucosa  of  the  nose  and  gastrointestinal  tract.  Epistaxis  is  the  most  common  problem.  The  presence  of  arteriovenous  malformations  is  predominant  in  the  lungs  (50%),  liver  (30-70%),  and  the  brain  (10%),  with  a  very  small  proportion  (<1%)  in  the  spinal  cord.  
SN  - 
PB  - McGraw-Hill Education
CY  - New York, NY
Y2  - 2024/04/18
UR  - accesspediatrics.mhmedical.com/content.aspx?aid=1164072553
ER  -