TY - CHAP M1 - Book, Section TI - Kartagener Syndrome A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas Y1 - 2019 N1 - T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - It is genetically transmitted autosomal dominant disease normally called “Primary Ciliary Dyskinesia” when it only includes the ciliopathic disease. It is characterized by chronic recurrent respiratory infections, sinusitis, bronchitis, pneumonia, and otitis media. However, in the presence of bronchiectasis, situs inversus, and chronic sinusitis, it is known as Kartagener Syndrome. The situs inversus is present only in 50% of primary ciliary dyskinesia cases. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/28 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1164074760 ER -