TY - CHAP M1 - Book, Section TI - Kostmann Syndrome A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas Y1 - 2019 N1 - T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - This is a rare blood disorder characterized by severe chronic neutropenia as a result of bone marrow primary insufficiency. Symptoms associated with this severe chronic neutropenia include recurring infections, severe fever, mouth ulcerations, and periodontitis. Life-threatening recurrent infections are common complications that may last for months or years and can affect both children and adults. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/04/19 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1164075680 ER -