TY - CHAP M1 - Book, Section TI - Mastocytosis A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas Y1 - 2019 N1 - T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - It is a medical condition that leads to accumulation and degranulation of mast cells (mastocytosis) in the skin, bone marrow, liver, spleen, gastrointestinal tract, and lymph nodes. Systemic mastocytosis occurs in approximately 10% of all cases. There are seven subtypes of this disorder based on the clinical presentation, the onset of the symptoms, and the prognosis (see below). The frequency of perioperative anaphylaxis appears to be higher in mastocytosis patients than in the general population. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/28 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1164077951 ER -