TY - CHAP M1 - Book, Section TI - Schilder Syndrome A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas Y1 - 2019 N1 - T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - A rare, progressive, and lethal disease of the central nervous system that affects mostly children and characterized by adrenal atrophy and diffuse central demyelination. Presents with progressive dementia, spasticity, cortical blindness, deafness, hemiplegia, quadriplegia, ataxia, pyramidal signs, retrobulbar neuritis, and pseudobulbar palsy. Seizures. Onset in late childhood. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/11/11 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1164084446 ER -