TY - CHAP M1 - Book, Section TI - Uhl Anomaly A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas Y1 - 2019 N1 - T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - An extremely rare congenital heart defect characterized by a near total absence of the myocardium of the parietal wall of the right ventricle resulting in severe dilatation and early congestive cardiac failure. Increased right heart volumes, severe diffuse hypokinesis, and tricuspid valve regurgitation. Fatal without intervention. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/29 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1164087074 ER -