TY  - CHAP
M1  - Book, Section
TI  - Chapter 154. Disorders of Glycogen Metabolism
A1  - Kishnani, Priya S.
A1  - Chen, Yuan-Tsong
A2  - Rudolph, Colin D.
A2  - Rudolph, Abraham M.
A2  - Lister, George E.
A2  - First, Lewis R.
A2  - Gershon, Anne A.
Y1  - 2011
N1  - 
T2  - Rudolph's Pediatrics, 22e
AB  - Glycogen,  the  storage  form  of  glucose  in  animal  cells,  is  composed  of  glucose  residues  joined  in  straight  chains  by  α–1,4  linkages  and  branched  at  intervals  of  4  to  10  residues  with  α–1,6  linkages.  The  treelike  molecule  can  have  a  molecular  weight  of  many  millions  and  may  aggregate  to  form  structures  recognizable  by  electron  microscopy.  In  muscle,  glycogen  forms  β  particles,  which  are  spherical  and  contain  up  to  60,000  glucose  residues.  Each  β  particle  contains  a  covalently  linked  protein  called  glycogenin.  Liver  contains  β  particles  and  rosettes  of  glycogen  called  α  particles,  which  appear  to  be  aggregated  β  particles.  
SN  - 
PB  - The McGraw-Hill Companies
CY  - New York, NY
Y2  - 2024/04/19
UR  - accesspediatrics.mhmedical.com/content.aspx?aid=6726054
ER  -