TY - CHAP M1 - Book, Section TI - Section 5. Primary Bullous Dermatoses A1 - Kane, Kay Shou-Mei A1 - Lio, Pater A. A1 - Stratigos, Alexander J. A1 - Johnson, Richard Allen Y1 - 2009 N1 - T2 - Color Atlas & Synopsis of Pediatric Dermatology, 2e AB - Epidermolysis bullosa (EB) defines a group of rare inherited mechanobullous skin disorders that are characterized by skin fragility and bullae formation. There are three forms of the disease: EB simplex, junctional EB, and dystrophic EB with over 20 different phenotypes representing mutations in the genes of at least 7 structural proteins of the skin (in the epidermis, dermal—epidermal junction, or upper papillary dermis). SN - PB - The McGraw-Hill Companies CY - New York, NY Y2 - 2022/08/11 UR - accesspediatrics.mhmedical.com/content.aspx?aid=56167126 ER -