TY - CHAP M1 - Book, Section TI - Benign Myoclonic Epilepsy in Infancy A1 - Connolly, Mary B. A2 - Duchowny, Michael A2 - Cross, J. Helen A2 - Arzimanoglou, Alexis PY - 2017 T2 - Pediatric Epilepsy AB - Benign myoclonic epilepsy in infancy (BMEI), first described by Dravet and Bureau in 1981, is a rare epilepsy syndrome.1 It is classified among the idiopathic generalized epilepsies and typically begins by the age of 3 years.2 BMEI is characterized by brief myoclonic seizures without other seizure types in developmentally normal children. The myoclonic seizures may occur spontaneously or be provoked by contact or noise. A history of simple febrile seizures may be present. In a series of 88 patients with BMEI, 26.1% had a history of simple febrile seizures.3 There is a family history of epilepsy or febrile seizures in 50% or more of patients. Myoclonic seizures are easily controlled with medication and usually remit later in childhood. Generalized tonic–clonic seizures may occur in late childhood or adolescence. Neurodevelopmental outcome is variable; most children have normal development but may experience educational difficulties. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/28 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1138409959 ER -