TY - CHAP M1 - Book, Section TI - Dandy-Walker Malformation A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas PY - 2019 T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - It is classified as a rare congenital human brain anomaly of the cerebellum and fourth ventricle. It is characterized by hypoplasia of the cerebellum, absence of the cerebellar vermis, and consequently noncommunicating hydrocephalus that is caused by cystic expansion of the fourth ventricle in the posterior fossa. The clinical features include abnormal motor coordination, raised intracranial pressure due to accumulation of the cerebrospinal fluid, and other multiple brain function problems. It is typically a lifelong disorder. Other systemic malformations are reported between 47 and 81% of DWS patients and include urogenital, renal, cardiac, intestinal, and craniofacial defects. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/10/08 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1164067470 ER -