TY  - CHAP
M1  - Book, Section
TI  - Ectrodactyly
A1  - Bissonnette, Bruno
A1  - Luginbuehl, Igor
A1  - Engelhardt, Thomas
PY  - 2019
T2  - Syndromes: Rapid Recognition and Perioperative Implications, 2e
AB  - This  is  a  congenital  limb  malformation  involving  the  central  rays  of  the  hands  or  feet.  Ectrodactyly  (derived  from  Greek  ektroma  [abortion]  and  daktylos  [finger])  refers  to  a  situation  where  at  least  one  entire  digit  (both  metacarpal/metatarsal  and  phalanges)  is  missing.  It  is  a  nonspecific  term  applied  to  a  variety  of  malformations.  The  usual  presentation  is  the  absence  of  the  third  digit  that  creates  a  cone-shaped  cleft  that  tapers  in  toward  the  wrist  and  divides  the  hand  into  two  parts.  The  resulting  deformation  resembles  a  lobster  claw.  Affected  individuals  have  normal  life  spans  and  intelligence.  It  is  important  not  to  confound  the  “atypical  cleft  hand,”  referred  to  as  symbrachydactyly  as  part  of  the  Ectrodactyly  Syndrome.  It  is  not  a  subtype  of  the  Cleft  Hand  Syndrome.  
SN  - 
PB  - McGraw-Hill Education
CY  - New York, NY
Y2  - 2024/04/18
UR  - accesspediatrics.mhmedical.com/content.aspx?aid=1164068710
ER  -