TY  - CHAP
M1  - Book, Section
TI  - Immotile Cilia Syndrome
A1  - Bissonnette, Bruno
A1  - Luginbuehl, Igor
A1  - Engelhardt, Thomas
PY  - 2019
T2  - Syndromes: Rapid Recognition and Perioperative Implications, 2e
AB  - It  is  a  rare  disorder  that  causes  defects  in  the  action  of  cilia  lining  the  respiratory  tract,  sinuses,  Eustachian  tube,  middle  ear,  fallopian  tube,  and  the  flagella  of  sperm  cells.  This  genetic  disorder  characterized  by  immotility  of  the  cilia  as  a  result  of  lack  or  dysfunctional  dynein.  Clinically,  these  patients  are  subjected  to  recurrent  respiratory  infections,  bronchiectasis,  and  sinusitis  as  a  result  of  accumulation  of  secretions.  This  anomaly  is  associated  in  approximately  50%  of  patients  affected  with  situs  inversus  (this  syndrome  is  often  called  Kartagener  Syndrome).  
SN  - 
PB  - McGraw-Hill Education
CY  - New York, NY
Y2  - 2024/04/19
UR  - accesspediatrics.mhmedical.com/content.aspx?aid=1164073738
ER  -