TY - CHAP M1 - Book, Section TI - Juvenile Intestinal Polyposis Syndrome A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas PY - 2019 T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - It is a familial noncancerous polyposis of the colon characterized by abdominal pain, rectal bleeding, and diarrhea. People with this medical condition typically develop polyps before age 20. Approximately 15% of those affected with this condition present other abnormalities such as intestinal malrotation, heart or brain defects, cleft palate, polydactyly of the hands and toes, and urogenital abnormalities. It is estimated that people with Juvenile Polyposis Syndrome have between 10 and 50% risk of developing a malignancy of the gastrointestinal tract. Colorectal cancer is the most common type. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/11/02 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1164074468 ER -