TY - CHAP M1 - Book, Section TI - Klippel-Trénaunay Syndrome A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas PY - 2019 T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - It is a rare congenital medical condition characterized by the association of soft tissue and bony hypertrophy, venous malformations, lymphatic abnormalities, and cutaneous capillary malformations. The main characteristics that confirm the diagnosis are port-wine stains (pathognomonic), venous and lymphatic malformations, and soft-tissue hypertrophy of the affected limb. Patients affected with large arteriovenous malformations may be at risk of peripheral thrombosis causing potentially a pulmonary embolism. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/04/16 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1164075502 ER -