TY - CHAP M1 - Book, Section TI - Limb-Girdle Muscular Dystrophy (LGMD) A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas PY - 2019 T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - Genetically transmitted neuromuscular disorder characterized by progressive proximal muscle weakness. It is characterized by a progressive muscle wasting that affects predominantly hip and shoulder muscles. The muscle weakness is generally symmetric, solely proximal, and very slow in progression. The age of onset is variable as it can be seen in childhood, adolescence, or young adulthood. However, it is usually established between 10 and 30 years of age. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/04/16 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1164076989 ER -