TY - CHAP M1 - Book, Section TI - West Syndrome A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas PY - 2019 T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - A disorder characterized by the triad of infantile spasms, an interictal EEG pattern termed hypsarrhythmia, and mental retardation. Most affected patients develop cerebral palsy, facial malformations, and skeletal deformities. The characteristic of the disease resides in the description of the spasms, which is described as violent jackknife or “salaam” movements where the whole body bends in half. The onset is during infancy. It is also observed in childhood where it is called “epileptic spasms” rather than infantile spasms. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/10/08 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1164088021 ER -