TY - CHAP M1 - Book, Section TI - Williams-Campbell Syndrome A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas PY - 2019 T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - It is a Congenital Cystic Bronchiectasis Syndrome caused by a defect of cartilage of the first and second generation bronchi leading to complete collapse of the lungs during expiration. The clinical feature is the presence of severe bronchomalacia. Respiratory symptoms can be severe and can be life-threatening. The differential diagnosis of congenital or acquired cystic bronchiectasis includes cystic fibrosis, ciliary dyskinesia, α1-antitripsin deficiency, immunoglobulin deficiency, autoimmune disease, and allergic bronchopulmonary aspergillosis. Also, see “Other conditions to be considered.” SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/10/03 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1164088158 ER -