TY - CHAP M1 - Book, Section TI - Gastrointestinal Polyps/Intestinal Cancer A1 - Chernoguz, Artur A1 - Frischer, Jason S. A2 - Ziegler, Moritz M. A2 - Azizkhan, Richard G. A2 - Allmen, Daniel von A2 - Weber, Thomas R. PY - 2014 T2 - Operative Pediatric Surgery, 2e AB - Presence of colorectal adenomas in children mandates evaluation for familial polyposis syndromes.The first presenting symptoms of polyposis syndromes are often secondary to extraintestinal manifestations and unrelated to gastrointestinal polyps.Polyposis syndrome treatment involves a number of surgical options which allow patients to maintain satisfactory lifestyles.Despite a number of surgical options, including total colectomy, cancer risks remain, and lifetime surveillance is mandatory.With improved survival, surveillance for extraintestinal manifestations is critical.Small intestinal malignancies are rare, but diagnosis in the pediatric population is often delayed secondary to low suspicion.Colorectal cancer in the pediatric population is extremely rare, but children with polyposis syndromes are at an extremely high risk of eventually developing colorectal cancer. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/28 UR - accesspediatrics.mhmedical.com/content.aspx?aid=1100439662 ER -