RT Book, Section A1 Hoffmann, Georg F. A1 Burlina, Alberto A1 Barshop, Bruce A. A2 Sarafoglou, Kyriakie A2 Hoffmann, Georg F. A2 Roth, Karl S. SR Print(0) ID 1140316466 T1 Organic Acidurias T2 Pediatric Endocrinology and Inborn Errors of Metabolism, 2e YR 2017 FD 2017 PB McGraw-Hill Education PP New York, NY SN 9780071773140 LK accesspediatrics.mhmedical.com/content.aspx?aid=1140316466 RD 2024/04/16 AB Organic acids occur as physiological intermediates in a variety of intracellular metabolic pathways, such as catabolism of amino acids, mitochondrial β-oxidation of fatty acids, tricarboxylic acid cycle, and cholesterol and fatty acid biosynthesis (Figure 14-1).