RT Book, Section A1 Hay, Jr, William W. A1 Levin, Myron J. A1 Deterding, Robin R. A1 Abzug, Mark J. SR Print(0) ID 1145455126 T1 Disaccharidase Deficiency T2 Quick Medical Diagnosis & Treatment Pediatrics YR 2017 FD 2017 PB McGraw-Hill Education PP New York, NY SN 9781264257614 LK accesspediatrics.mhmedical.com/content.aspx?aid=1145455126 RD 2024/04/24 AB Characteristics of primary disaccharidase deficiency includePermanent disaccharide intoleranceAbsence of intestinal injuryFrequent positive family historyTransient secondary disaccharidase deficiency may be caused by mucosal damage, such as from acute viral enteritisGenetic lactase deficiency develops inVirtually all Asians, Alaskan natives, and Native Americans80% of Africans70% of African Americans30–60% of white AmericansCongenital lactase deficiency is extremely rareSucrase-isomaltase deficiencyInherited in an autosomal recessive fashionMost common in Greenland, Iceland, and among Alaskan nativesCondition is rare in other groups