RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Engelhardt, Thomas
SR Print(0)
ID 1164059988
T1 Achalasia-Alacrima Syndrome
T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e
YR 2019
FD 2019
PB McGraw-Hill Education
PP New York, NY
SN 9781259861789
LK accesspediatrics.mhmedical.com/content.aspx?aid=1164059988
RD 2024/04/23
AB This  inherited  disorder  is  most  likely  a  variant  of  ☞Allgrove  Syndrome  (Achalasia-Alacrima-Adrenocorticotropic  hormone  [ACTH]  Insensitivity  Syndrome;  Triple  A-Syndrome).  However,  in  a  small  minority  it  can  be  an  acquired  abnormality  induced  by  the  formation  of  antibodies  that  block  ACTH  receptors.  In  contrast  to  Addison  Syndrome,  the  renin-angiotensin-aldosterone  axis  functions  normally.