RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Engelhardt, Thomas
SR Print(0)
ID 1164061699
T1 Anderson-Tawil Syndrome (ATS)
T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e
YR 2019
FD 2019
PB McGraw-Hill Education
PP New York, NY
SN 9781259861789
LK accesspediatrics.mhmedical.com/content.aspx?aid=1164061699
RD 2024/04/17
AB An  inherited  disorder  characterized  by  the  clinical  triad  of  potassium-sensitive  periodic  flaccid  paralysis  (low,  normal,  or  high  potassium  levels),  ventricular  arrhythmias  (bigeminy,  long-QT  interval,  ectopy,  bidirectional  ventricular  tachycardia),  and  dysmorphic  facial  features.  Sudden  death  has  been  reported.  ATS  must  not  be  confused  with  Andersen  Disease  (☞Glycogen  Storage  Disease  Type  IV).