RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Engelhardt, Thomas
SR Print(0)
ID 1164066497
T1 Congenital Dyserythropoietic Anemias
T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e
YR 2019
FD 2019
PB McGraw-Hill Education
PP New York, NY
SN 9781259861789
LK accesspediatrics.mhmedical.com/content.aspx?aid=1164066497
RD 2024/04/24
AB This  is  a  group  of  inherited  disorders  characterized  by  quantitatively  and  qualitatively  altered  erythropoiesis  resulting  in  usually  mild-to-moderate  anemia.  Premature  destruction  of  erythroblasts  in  the  bone  marrow  reduces  their  numbers  reaching  maturity.  In  addition,  there  is  peripheral  destruction  of  these  dysplastic  erythroblasts.  Three  main  types  of  congenital  dyserythropoietic  anemia  (CDA  I-III)  and  four  other  extremely  rare  types  have  been  described.