RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Engelhardt, Thomas
SR Print(0)
ID 1164072904
T1 Herlyn-Werner-Wunderlich Syndrome
T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e
YR 2019
FD 2019
PB McGraw-Hill Education
PP New York, NY
SN 9781259861789
LK accesspediatrics.mhmedical.com/content.aspx?aid=1164072904
RD 2024/04/19
AB It  is  a  rare  genetic  disorder  characterized  by  the  presence  of  a  uterus  didelphys,  a  blind  hemivagina  and  ipsilateral  renal  agenesis.  Individuals  affected  may  have  either  completely  or  incompletely  obstructed  vaginal  septum.  The  most  common  presentation  is  acute  or  progressive  lower  abdominal  pain,  dysmenorrhea  (especially  in  Type  I),  and  abdominal  mass  in  the  lower  abdomen  secondary  to  hematocolpos  and/or  hematometra.