RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Engelhardt, Thomas
SR Print(0)
ID 1164072972
T1 HHHH Syndrome
T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e
YR 2019
FD 2019
PB McGraw-Hill Education
PP New York, NY
SN 9781259861789
LK accesspediatrics.mhmedical.com/content.aspx?aid=1164072972
RD 2024/04/19
AB HHHH  is  an  acronym  that  stands  for  Hereditary  Hemihypotrophy,  Hemiparesis,  and  Hemiathetosis.  It  is  characterized  by  congenital  unilateral  (left  or  right)  hemiparesis  with  subsequent  development  of  hemihypoplasia  and  athetoid  posturing  of  the  left  hand.  Other  clinical  features  include  hemiatrophy,  involuntary  movements,  and  seizures.  It  has  been  suggested  that  either  an  autosomal  dominant  or  X-linked  inheritance  is  likely.