RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Engelhardt, Thomas SR Print(0) ID 1164075202 T1 Ketoacidosis of Infancy T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e YR 2019 FD 2019 PB McGraw-Hill Education PP New York, NY SN 9781259861789 LK accesspediatrics.mhmedical.com/content.aspx?aid=1164075202 RD 2024/04/19 AB An inborn error of ketone body catabolism resulting in intermittent episodes of ketoacidosis. The potential presence of cerebral edema, raised intracranial pressure, vomiting, and tachypnea makes this medical condition a serious clinical problem requiring immediate attention. There is no evidence that it is associated, as in older patients, with an uncontrolled diabetes mellitus.