RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Engelhardt, Thomas SR Print(0) ID 1164075502 T1 Klippel-Trénaunay Syndrome T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e YR 2019 FD 2019 PB McGraw-Hill Education PP New York, NY SN 9781259861789 LK accesspediatrics.mhmedical.com/content.aspx?aid=1164075502 RD 2024/03/28 AB It is a rare congenital medical condition characterized by the association of soft tissue and bony hypertrophy, venous malformations, lymphatic abnormalities, and cutaneous capillary malformations. The main characteristics that confirm the diagnosis are port-wine stains (pathognomonic), venous and lymphatic malformations, and soft-tissue hypertrophy of the affected limb. Patients affected with large arteriovenous malformations may be at risk of peripheral thrombosis causing potentially a pulmonary embolism.