RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Engelhardt, Thomas SR Print(0) ID 1164078668 T1 Microgastria-Limb Reduction Defects Association T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e YR 2019 FD 2019 PB McGraw-Hill Education PP New York, NY SN 9781259861789 LK accesspediatrics.mhmedical.com/content.aspx?aid=1164078668 RD 2024/03/28 AB It is a very rare syndrome characterized by asplenia, microgastria, hypoplastic arm, hand, and wrist or absent upper limb. Severe congenital heart defect (eg, truncus arteriosus) as well as pulmonary and kidney anomalies can be present. The treatment involves reconstructive gastric surgery (Hunt-Lawrence pouch) to help improve the child’s feeding abilities.