RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Engelhardt, Thomas SR Print(0) ID 1164078693 T1 Microvillous Inclusion Syndrome T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e YR 2019 FD 2019 PB McGraw-Hill Education PP New York, NY SN 9781259861789 LK accesspediatrics.mhmedical.com/content.aspx?aid=1164078693 RD 2024/03/28 AB It is an extremely rare inherited enteropathy that is typically apparent within hours or days after birth. The disorder is characterized by chronic, severe, watery diarrhea, and malabsorption caused by hypoplasia and/or atrophy of the wall of the small intestine (eg, hypoplastic villus atrophy, defective brush-border assembly and differentiation). In infants, chronic diarrhea and malabsorption may result in severe dehydration, electrolyte imbalance, malnutrition, failure to thrive, and acidosis.