RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Engelhardt, Thomas
SR Print(0)
ID 1164084446
T1 Schilder Syndrome
T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e
YR 2019
FD 2019
PB McGraw-Hill Education
PP New York, NY
SN 9781259861789
LK accesspediatrics.mhmedical.com/content.aspx?aid=1164084446
RD 2024/04/19
AB A  rare,  progressive,  and  lethal  disease  of  the  central  nervous  system  that  affects  mostly  children  and  characterized  by  adrenal  atrophy  and  diffuse  central  demyelination.  Presents  with  progressive  dementia,  spasticity,  cortical  blindness,  deafness,  hemiplegia,  quadriplegia,  ataxia,  pyramidal  signs,  retrobulbar  neuritis,  and  pseudobulbar  palsy.  Seizures.  Onset  in  late  childhood.