RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Engelhardt, Thomas
SR Print(0)
ID 1164087578
T1 Vogt-Vogt Syndrome
T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e
YR 2019
FD 2019
PB McGraw-Hill Education
PP New York, NY
SN 9781259861789
LK accesspediatrics.mhmedical.com/content.aspx?aid=1164087578
RD 2024/09/14
AB It  is  a  rare  extrapyramidal  genetic  disorder  characterized  by  double-sided  athetosis  occurring  in  early  childhood.  It  is  a  type  of  cerebral  palsy  manifesting  predominantly  as  bilateral  involuntary  movements,  beginning  by  the  age  3  years  and  usually  preceded  by  generalized  hypotonia,  and  delayed  motor  development  that  is  generally  associated  with  difficulty  in  maintaining  a  symmetrical  posture.  The  clinical  features  include  slow,  writhing,  purposeless  movements  mainly  affecting  the  hands  and  face  (forced  laughter  and  crying).  Disturbance  of  posture  is  mainly  contractures  in  position  with  flexion  of  the  knees.  There  is  also  disturbance  of  tonus  with  over  stretchable  joint.  Besides  athetosis  spastic  and  cerebral  signs  also  occur.