RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Engelhardt, Thomas SR Print(0) ID 1164087763 T1 Wagner Syndrome T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e YR 2019 FD 2019 PB McGraw-Hill Education PP New York, NY SN 9781259861789 LK accesspediatrics.mhmedical.com/content.aspx?aid=1164087763 RD 2024/03/28 AB This is a rare inherited vitreoretinopathy characterized by many optical malformations (eg, ensheathed retinal vessels, retinal pigmentation, circular membranes in a liquefied vitreous, choroidal atrophy) with a progressive clinical course that ends with optic atrophy and blindness. Other features include light-sensitive tissue that lines the retina, cataracts, and glaucoma. These may cause retinal detachment. Patients with unexplained early onset cataract or retinal detachment should be carefully evaluated for vitreoretinal degeneration. Often misdiagnosed for Stickler Syndrome; however, lacks the systemic features and the high incidence of retinal detachment seen with this latter condition differs between both disorders.