RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Engelhardt, Thomas SR Print(0) ID 1164088021 T1 West Syndrome T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e YR 2019 FD 2019 PB McGraw-Hill Education PP New York, NY SN 9781259861789 LK accesspediatrics.mhmedical.com/content.aspx?aid=1164088021 RD 2024/10/03 AB A disorder characterized by the triad of infantile spasms, an interictal EEG pattern termed hypsarrhythmia, and mental retardation. Most affected patients develop cerebral palsy, facial malformations, and skeletal deformities. The characteristic of the disease resides in the description of the spasms, which is described as violent jackknife or “salaam” movements where the whole body bends in half. The onset is during infancy. It is also observed in childhood where it is called “epileptic spasms” rather than infantile spasms.