RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Engelhardt, Thomas
SR Print(0)
ID 1164088158
T1 Williams-Campbell Syndrome
T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e
YR 2019
FD 2019
PB McGraw-Hill Education
PP New York, NY
SN 9781259861789
LK accesspediatrics.mhmedical.com/content.aspx?aid=1164088158
RD 2024/04/19
AB It  is  a  Congenital  Cystic  Bronchiectasis  Syndrome  caused  by  a  defect  of  cartilage  of  the  first  and  second  generation  bronchi  leading  to  complete  collapse  of  the  lungs  during  expiration.  The  clinical  feature  is  the  presence  of  severe  bronchomalacia.  Respiratory  symptoms  can  be  severe  and  can  be  life-threatening.  The  differential  diagnosis  of  congenital  or  acquired  cystic  bronchiectasis  includes  cystic  fibrosis,  ciliary  dyskinesia,  α1-antitripsin  deficiency,  immunoglobulin  deficiency,  autoimmune  disease,  and  allergic  bronchopulmonary  aspergillosis.  Also,  see  “Other  conditions  to  be  considered.”