RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Engelhardt, Thomas SR Print(0) ID 1164088158 T1 Williams-Campbell Syndrome T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e YR 2019 FD 2019 PB McGraw-Hill Education PP New York, NY SN 9781259861789 LK accesspediatrics.mhmedical.com/content.aspx?aid=1164088158 RD 2024/10/08 AB It is a Congenital Cystic Bronchiectasis Syndrome caused by a defect of cartilage of the first and second generation bronchi leading to complete collapse of the lungs during expiration. The clinical feature is the presence of severe bronchomalacia. Respiratory symptoms can be severe and can be life-threatening. The differential diagnosis of congenital or acquired cystic bronchiectasis includes cystic fibrosis, ciliary dyskinesia, α1-antitripsin deficiency, immunoglobulin deficiency, autoimmune disease, and allergic bronchopulmonary aspergillosis. Also, see “Other conditions to be considered.”